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Repair of pulmonary atresia with ventricular septal defect (VSD) is a complex surgical procedure aimed at correcting a congenital heart defect where the pulmonary valve does not develop properly, leading to an obstruction of blood flow from the right ventricle to the lungs. In this condition, the heart's ability to deliver oxygenated blood to the body is compromised. The presence of a VSD, which is an abnormal opening in the septum separating the right and left ventricles, further complicates the situation by allowing blood to flow between the two ventricles. This procedure is specifically designed for patients who exhibit both pulmonary atresia and a VSD, and it requires careful planning and execution due to the variability in the anatomical presentation of each patient. The surgical approach is often tailored to the individual, and the repair may be performed in stages, depending on the severity of the defects and the overall health of the patient. The procedure involves accessing the heart through a median sternotomy, harvesting a patch of pericardium for grafting, and establishing cardiopulmonary bypass to facilitate the repair. The surgeon evaluates the anatomy of the pulmonary artery and its branches to determine the best site for constructing or replacing a conduit that will allow blood to flow from the ventricle to the pulmonary artery, thereby restoring proper circulation to the lungs.
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The procedure is indicated for patients diagnosed with:
The surgical procedure involves several critical steps to ensure the successful repair of pulmonary atresia with VSD:
Post-procedure care involves monitoring the patient for any complications and ensuring proper recovery. Patients may require intensive care following the surgery to manage their recovery effectively. The placement of chest tubes is common to facilitate drainage and prevent fluid accumulation. The healthcare team will monitor vital signs, cardiac function, and overall recovery progress. Follow-up appointments will be necessary to assess the success of the repair and to plan any further interventions if needed.
| Short Descr | REPAIR PULMONARY ATRESIA | Medium Descr | RPR PULMONARY ATRESIA W/CONSTJ/RPLCMT CONDUIT | Long Descr | Repair of pulmonary atresia with ventricular septal defect, by construction or replacement of conduit from right or left ventricle to pulmonary artery | Status Code | Active Code | Global Days | 090 - Major Surgery | PC/TC Indicator (26, TC) | 0 - Physician Service Code | Multiple Procedures (51) | 2 - Standard payment adjustment rules for multiple procedures apply. | Bilateral Surgery (50) | 0 - 150% payment adjustment for bilateral procedures does NOT apply. | Physician Supervisions | 09 - Concept does not apply. | Assistant Surgeon (80, 82) | 2 - Payment restriction for assistants at surgery does not apply to this procedure... | Co-Surgeons (62) | 1 - Co-surgeons could be paid, though supporting documentation is required... | Team Surgery (66) | 0 - Team surgeons not permitted for this procedure. | Diagnostic Imaging Family | 99 - Concept Does Not Apply | APC Status Indicator | Inpatient Procedures, not paid under OPPS | Type of Service (TOS) | 2 - Surgery | Berenson-Eggers TOS (BETOS) | P2F - Major procedure, cardiovascular-Other | MUE | 1 | CCS Clinical Classification | 43 - Heart valve procedures |
This is a primary code that can be used with these additional add-on codes.
| 33257 | Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), limited (eg, modified maze procedure) (List separately in addition to code for primary procedure) | 33259 | Addon Code MPFS Status: Active Code APC C Illustration for Code Operative tissue ablation and reconstruction of atria, performed at the time of other cardiac procedure(s), extensive (eg, maze procedure), with cardiopulmonary bypass (List separately in addition to code for primary procedure) | 33924 | Addon Code MPFS Status: Active Code APC C CPT Assistant Article Ligation and takedown of a systemic-to-pulmonary artery shunt, performed in conjunction with a congenital heart procedure (List separately in addition to code for primary procedure) | 34714 | Addon Code MPFS Status: Active Code APC N ASC N1 Open femoral artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by groin incision, unilateral (List separately in addition to code for primary procedure) | 34716 | Addon Code MPFS Status: Active Code APC N ASC N1 Open axillary/subclavian artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by infraclavicular or supraclavicular incision, unilateral (List separately in addition to code for primary procedure) | 34833 | Addon Code Resequenced Code MPFS Status: Active Code APC C CPT Assistant Article Open iliac artery exposure with creation of conduit for delivery of endovascular prosthesis or for establishment of cardiopulmonary bypass, by abdominal or retroperitoneal incision, unilateral (List separately in addition to code for primary procedure) |
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| 1994-01-01 | Added | First appearance in code book in 1994. |
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