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Official Description

Repair, congenital arteriovenous fistula; head and neck

© Copyright 2026 American Medical Association. All rights reserved.

Common Language Description

A congenital arteriovenous fistula is a vascular anomaly characterized by an abnormal connection between an artery and a vein that is present from birth. This condition can manifest anywhere within the vascular system and can vary significantly in terms of size and length. The presence of this abnormal communication allows blood to flow from the artery into the vein under high pressure. Since the walls of veins are not designed to withstand such high-pressure blood flow, they can become stretched and enlarged over time. This enlargement can lead to an increased volume of blood flowing into the venous component, which may result in various cardiovascular complications. Repairing congenital arteriovenous fistulas can be particularly challenging due to their potential extension into surrounding anatomical structures. To facilitate the repair process, a separate angiography may be performed to clearly outline the path of the fistula. The surgical procedure involves exposing the fistula, carefully dissecting it from adjacent tissues, and placing clamps on both the artery and vein to isolate the fistula. The abnormal connection is then severed, and the artery and vein are repaired, either with sutures or by using a synthetic patch or vein graft. After ensuring hemostasis, the overlying tissues are closed in layers. This procedure is specifically coded as CPT® Code 35180 for repairs located in the head and neck region, with different codes designated for repairs in the thorax, abdomen, and extremities.

© Copyright 2026 Coding Ahead. All rights reserved.

1. Indications

The procedure for repairing a congenital arteriovenous fistula is indicated in the following situations:

  • Congenital arteriovenous fistula Present at birth, this condition requires intervention to prevent complications associated with abnormal blood flow.
  • Cardiovascular complications The abnormal communication can lead to various cardiovascular issues, necessitating repair to restore normal blood flow dynamics.
  • Enlargement of venous walls The stretching of venous walls due to high-pressure arterial blood flow can lead to further complications, making surgical repair essential.

2. Procedure

The procedure for repairing a congenital arteriovenous fistula involves several critical steps:

  • Angiography Prior to the surgical repair, a separate angiography is performed to delineate the course of the arteriovenous fistula. This imaging technique provides essential information about the anatomy and extent of the fistula, guiding the surgical approach.
  • Exposure and dissection The surgeon then exposes the fistula by making an incision in the appropriate area. Careful dissection is performed to free the fistula from surrounding tissues, ensuring that the surgical field is clear for the repair.
  • Clamping Once the fistula is adequately exposed, clamps are placed on both the artery and vein. This step is crucial as it isolates the fistula, preventing blood flow during the repair process.
  • Severing the fistula The abnormal communication between the artery and vein is then severed. This step is essential to eliminate the high-pressure flow from the artery into the vein.
  • Repairing the vessels After severing the fistula, the surgeon repairs the artery and vein. This can be accomplished using sutures to close the vessels directly, or alternatively, a synthetic patch or vein graft may be employed to facilitate the repair.
  • Checking hemostasis Once the repairs are made, the clamps are removed, and the surgeon checks for hemostasis to ensure that there is no bleeding at the repair site.
  • Closure of overlying tissues Finally, the overlying tissues are closed in layers to complete the procedure, ensuring proper healing and minimizing scarring.

3. Post-Procedure

After the repair of a congenital arteriovenous fistula, patients typically require monitoring for any signs of complications, such as bleeding or infection. The recovery process may involve pain management and follow-up appointments to assess the success of the repair and the overall vascular health. Patients may also be advised on activity restrictions during the initial recovery phase to promote healing and prevent strain on the surgical site.

Short Descr RPR CGEN AV FISTULA HEAD&NCK
Medium Descr REPAIR CONGENITAL AV FISTULA HEAD & NECK
Long Descr Repair, congenital arteriovenous fistula; head and neck
Status Code Active Code
Global Days 090 - Major Surgery
PC/TC Indicator (26, TC) 0 - Physician Service Code
Multiple Procedures (51) 2 - Standard payment adjustment rules for multiple procedures apply.
Bilateral Surgery (50) 0 - 150% payment adjustment for bilateral procedures does NOT apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 2 - Payment restriction for assistants at surgery does not apply to this procedure...
Co-Surgeons (62) 1 - Co-surgeons could be paid, though supporting documentation is required...
Team Surgery (66) 0 - Team surgeons not permitted for this procedure.
Diagnostic Imaging Family 99 - Concept Does Not Apply
APC Status Indicator Hospital Part B services paid through a comprehensive APC
Type of Service (TOS) 2 - Surgery
Berenson-Eggers TOS (BETOS) P2F - Major procedure, cardiovascular-Other
MUE 2
CCS Clinical Classification 59 - Other OR procedures on vessels of head and neck
GX Notice of liability issued, voluntary under payer policy
Date
Action
Notes
2025-01-01 Changed Short Description changed.
2013-01-01 Changed Medium Descriptor changed.
Pre-1990 Added Code added.
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