CPT® Code 49611

An omphalocele is a congenital defect characterized by a failure of the abdominal wall to close properly, resulting in the protrusion of intra-abdominal organs through the abdominal wall at the umbilical ring. This defect is marked by the absence of abdominal muscles, fascia, and skin, with the protruding structures being covered by a membrane composed of peritoneum and amnion. The classic presentation of an omphalocele involves the umbilical cord being attached to the sac that contains the herniated organs. The surgical repair of an omphalocele is typically performed in two stages. The first stage involves the ligation of umbilical vessels, amputation of the umbilical cord, and the creation of skin flaps to cover the defect, which results in a large ventral hernia. The second stage, which is denoted by CPT® Code 49611, is performed at a later date, usually between six months to two years after the initial repair. During this stage, the previously created skin flaps are reopened, and the ventral hernia is repaired, restoring the integrity of the abdominal wall.