ICD-9-CM Code 277.87

Disorders of mitochondrial metabolism
Kearns-Sayre syndrome
Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes (MELAS syndrome)
Mitochondrial Neurogastrointestinal Encephalopathy syndrome (MNGIE)
Myoclonus with Epilepsy and with Ragged Red Fibers (MERRF syndrome)
Neuropathy, Ataxia and Retinitis Pigmentosa (NARP syndrome)
Use additional code for associated conditions
Excludes: disorders of pyruvate metabolism (271.8), Leber's optic atrophy (377.16), Leigh's subacute necrotizing encephalopathy (330.8), Reye's syndrome (331.81)