CPT® Code 33619

Repair of single ventricle with aortic outflow obstruction and aortic arch hypoplasia (hypoplastic left heart syndrome) (eg, Norwood procedure)

The CPT® Code 33619 refers to the surgical procedure known as the Norwood procedure, which is specifically designed to address hypoplastic left heart syndrome (HLHS). This congenital cardiac anomaly is characterized by the underdevelopment of the left ventricle and aortic arch, leading to a single ventricle that cannot effectively support both systemic and pulmonary circulations. In HLHS, the pulmonary artery must compensate by supplying blood to both the lungs and the body, which creates a significant imbalance in blood flow. The Norwood procedure is a critical intervention aimed at correcting this imbalance and establishing a more effective circulation. The surgery involves a series of complex steps, including median sternotomy to access the heart, the establishment of cardiopulmonary bypass, and the use of hypothermic circulatory arrest to protect the brain and other vital organs during the procedure. The surgical team meticulously excises the atrial septum, ligates and removes the ductus arteriosus, and reconstructs the aortic arch using grafts to ensure adequate blood flow. This procedure is essential for improving the quality of life and survival rates in infants diagnosed with this serious condition.