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Official Description

Mucopolysaccharides, acid, quantitative

© Copyright 2026 American Medical Association. All rights reserved.

Common Language Description

The CPT® Code 83864 refers to a quantitative test for acid mucopolysaccharides, which are also known as glycosaminoglycans (GAGs). These are long-chain sugar molecules that play a crucial role in the structure and function of various tissues in the body, including bone, connective tissue, and joint fluid. The test is primarily conducted on a urine sample to assess the levels of these mucopolysaccharides. Conditions such as mucopolysaccharidosis (MPS) arise from genetically inherited metabolic syndromes, including Hunter syndrome, Hurler syndrome, Sanfilippo syndrome, Scheie syndrome, and Morquio syndrome. These syndromes are characterized by a deficiency of specific enzymes that are responsible for breaking down the sugar molecule chains, leading to an accumulation of mucopolysaccharides in the body. The quantitative test indicated by CPT® Code 83864 is particularly important for monitoring patients who have already been diagnosed with MPS, as it helps in tracking the levels of GAGs over time. For optimal results, a urine specimen is typically collected as the first morning void, although a 24-hour urine specimen may also be utilized. The analysis of the urine sample is performed using spectrophotometry, a method that measures the intensity of light absorbed by the sample, providing a quantitative assessment of the acid mucopolysaccharide levels present.

© Copyright 2026 Coding Ahead. All rights reserved.

1. Indications

The acid mucopolysaccharide test, represented by CPT® Code 83864, is indicated for the following conditions:

  • Monitoring Mucopolysaccharidosis (MPS) This test is performed to monitor the levels of glycosaminoglycans (GAGs) in patients who have been previously diagnosed with various forms of mucopolysaccharidosis, ensuring that any changes in their condition can be tracked effectively.
  • Diagnosis of Genetic Metabolic Syndromes The test may also be utilized in the diagnostic process for genetic metabolic syndromes such as Hunter syndrome, Hurler syndrome, Sanfilippo syndrome, Scheie syndrome, and Morquio syndrome, which are characterized by enzyme deficiencies affecting mucopolysaccharide metabolism.

2. Procedure

The procedure for conducting the acid mucopolysaccharide test involves several key steps:

  • Specimen Collection A urine specimen is collected from the patient, with the first morning void being the preferred sample. This timing is crucial as it typically provides a more concentrated sample of urine, which can yield more accurate results. Alternatively, a 24-hour urine specimen may be collected to ensure a comprehensive assessment of mucopolysaccharide levels over an entire day.
  • Sample Preparation Once the urine specimen is obtained, it is prepared for analysis. This may involve specific handling and storage conditions to preserve the integrity of the sample until testing can be performed.
  • Testing Methodology The quantitative analysis of the urine sample is conducted using spectrophotometry. This technique measures the amount of light absorbed by the sample at specific wavelengths, allowing for the quantification of acid mucopolysaccharides present in the urine.
  • Result Interpretation After the spectrophotometric analysis, the results are interpreted to determine the levels of acid mucopolysaccharides. These results are then compared to established reference ranges to assess whether the levels are within normal limits or indicative of a metabolic disorder.

3. Post-Procedure

After the acid mucopolysaccharide test is completed, the patient may not require any specific post-procedure care, as the test is non-invasive and does not involve any significant risks. However, it is essential for healthcare providers to communicate the results to the patient and discuss any necessary follow-up actions based on the findings. If elevated levels of mucopolysaccharides are detected, further diagnostic evaluations or referrals to specialists may be warranted to manage any underlying conditions effectively. Regular monitoring may also be recommended for patients with known mucopolysaccharidosis to track disease progression and treatment efficacy.

Short Descr MUCOPOLYSACCHARIDES
Medium Descr MUCOPOLYSACCHARIDES ACID QUANTITATIVE
Long Descr Mucopolysaccharides, acid, quantitative
Status Code Statutory Exclusion (from MPFS, may be paid under other methodologies)
Global Days XXX - Global Concept Does Not Apply
PC/TC Indicator (26, TC) 9 - Not Applicable
Multiple Procedures (51) 9 - Concept does not apply.
Bilateral Surgery (50) 9 - Concept does not apply.
Physician Supervisions 09 - Concept does not apply.
Assistant Surgeon (80, 82) 9 - Concept does not apply.
Co-Surgeons (62) 9 - Concept does not apply.
Team Surgery (66) 9 - Concept does not apply.
Diagnostic Imaging Family 99 - Concept Does Not Apply
CLIA Waived (QW) No
APC Status Indicator Conditionally packaged laboratory tests
Type of Service (TOS) 5 - Diagnostic Laboratory
Berenson-Eggers TOS (BETOS) T1H - Lab tests - other (non-Medicare fee schedule)
MUE 1
CCS Clinical Classification 233 - Laboratory - Chemistry and Hematology
90 Reference (outside) laboratory: when laboratory procedures are performed by a party other than the treating or reporting physician or other qualified health care professional, the procedure may be identified by adding modifier 90 to the usual procedure number.
Q4 Service for ordering/referring physician qualifies as a service exemption
Date
Action
Notes
2015-01-01 Changed Code description changed.
Pre-1990 Added Code added.
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